PKHL1_MOUSE Q80ZA4
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UniProt:Q80ZA4
Recommended name:Fibrocystin-L
EC number:
Alternative names:(Polycystic kidney and hepatic disease 1-like protein 1) (PKHD1-like protein 1) (Protein D86)
Cleaved into:
GeneID:192190
Gene names (primary ):Pkhd1l1
Gene names (synonym ):
Gene names (ORF ):
Length:4249
Mass:464732
Sequence:MGHLWLSGTWFLFGLLWCAADSHKGSSETIPKVTEVIPKYGSINGATRLTIKGEGFSQASQFNYGADNTELGNHVQLVSSFQSITCDVEKDSSHSTQITCYTRAMPEDTYSVRVSVDGVPVAENNTCKGVASSWACSFSTKSFRTPTIRSITPLSGTPGTLITIKGRLFTDVYGSNTALSSNGRNVRILRIYIGGMPCELLIPHSDDLYGLKLDHANGDTGSVTCKTTGTYIGHHNVSFILDSDYGRSFPEKMTYFVSSLNKISMFQTYPEVVMVSPSKGSTEGGTLLTIHGHFFDQTDLPVRVLVGGQACAILNVTENTIYCKTPPKPHILKATYPGGRGLKVEVWNNSRPAHLEDILEYNEHTPGYMGATWTDSASYVWPIEQDTFVARISGFLVPPDSDVYRFYIRGDDRYAIYFSQTGRTEDKVRIAYYSGNANTYFSNSTQRSDEIHLQKGKEYYIEILLQEYTLSAFVDVGLYQYKNVFTEQQTGDALNEEQVIKSQSTVVPEVQIITLENWETADVTNEVQQVTVTSPCVGANSCSLSQYRFIYNMEKTVWLPADASDFTLKSALNDLWSIKPDSVQVTSKRDLQSYIYTITFVSTRGDFDLLGYEVFEGSNVTLSITEQTKGKPNLETFTLNWDGIASKPLTPESSEAEFQVAVEEMVSAKCPPEIAHLEEGFLVKYFRDYETDFELEHINRGQKTAETDAYCGRYSLKNPAVLFDSTDVKPNKSPYGDILLFPYNQLCLAYKGSLANFIDLKFKYQDSGKIIRSADVQFEYNFASGNKWTYTCIDLLDFLQTKYAGTSFSLQRITLQKSSEFQSIYVDAVYIGQTPTVSVLDDMPKRRPPALANKGIFLKHFQVNRTKLNGSAMTIQYSVTITSYNCSHNIPMMAVSFGQIITNETKNELVYRGNNWPGESKIRIQKIQEASPPISGSFDVQAYGHTLKGIPAAVPAADLQFALQSLEEIEQVSVNREGTCAGYSWSIRWTSPRGKQPLLQINDSNIIGEKANVTVTTIKEGGLFRQRIPGDMLRTLNQQPQVEVYVNGIPAKCSGDCGFTWDAMITPLILTTTPSEGSYAESTILTIAGSGFSPTSAVSVSVGSTRCSLLSVEENEIKCQILNGSAGHVPVAVSIADVGLAQNLEGEGSHFIYRSQISHVWPDSGSLAGGTLLTISGFGFSENSTVLVGNETCNVIEGDLNRITCRTSKRIEGTVDISVITNGIQVTAKDSFSYSCLQTPVVTDFSPKERTVLGKVNLTIKGYNFGNELAQNTVYVGRKHCQVLHSNFTDITCLLPTLPPGKHDIYVKVRNWGLASTRNKLNASILYILEVIHMFPQRGSLYGGTEITIMGFGFSTIPTENSVLLGSFPCDITSSSENVIKCTLHSTGTVFRITNNGSHLVHGLGYAWSPSVLNVTVGDTVVWSWQAHPFLRGIGYRIFSVSSPGSVTYDDKGFTNGRQKSASGSFSYQFTSPGIYYYSSGYVDEAHSISLQGVINVFPAEARHIPLYLFVGNIEATYVPAGPAHLQLASTAAGCLATEPLCGLNDTRVKHSNKLFFELSNCISPSIINITPSTGTANELITIIGHGFSSLPCANKVTIGSYPCVVEESSENSIICHIDPQNSMNVGIREIVTLIVYNLGTAINTLTKAFDRRFVLLPNIDMVMPKAGSTTGMTRVTIQGSGFMSSPEGVEVFMGDFPCKVLSVTYTAIECETSPAPQQLVLVDILIHGVPAQCQSNCSFSYLENIAPYVTGIFPNSIQGYGNVLIKGERFGTVLEEISIFIGSQQFRVIDVNENNITVLMTPLEAGLHSLSVVVGSKGLALGNLTISSPAVASVSPTSGSIAGGTTLMITGNGFSPGNTTVTVGDQPCQITFISSSEVYCSTPAGRAGTANLKISVNAIIYPPLSFTYAMEDTPFLKRIIPNRGLPGTEVEITGSNLGFAISDVSVMIKESVCNVTTVNDTVLQCTVGEHAGGIFPVTMLHKTKGSAVSSVAFEYPLSIQNIYPTQGSFGGGQTLTVTGMGFDPWNSTILVCNSECAVDKLRSNSTTLFCVIPPNNGKGHDQVCGVSVVNGKDSSHSTKLFTYTLSLTPLITEISPRRGSTAGGTRLTVTGSGFSENTQGVQVFVGNSKCDIQYSNKTHIVCMTSVHVPSGWVPVHVNIKNIGLAKLENADFLYADVWSANSSWGGSPPPEEGSLAVITKGQIILLDQSTPILKMLLIQGGTLIFDEANIELQAENILITDGGVLQIGTEASPFQHRAVITLHGHLRSPELPVYGAKTLGVREGTLDLHGLPIPVVWTRLTHTANAGEWTLTVQEAVTWKAGDNIVIASTGHRHSQAENEKRTIASVSADGMHITLTKPLNYTHLGITTTLPDGTVFEARAEVGILTRNILIRGSDNVEWNDKIPSCPDGFDTGEFATQTCLQGKFGEEMGSDQFGGCIMLHAPLPGADMVTGRIEYVEVFHAGQSFRLGRYPIHWHLLGDLQFKSYVKGCAIHQSYNRAITIHNTHHLLVERNIIYDIKGGAFFIEDGIEHGNILQYNLAVFVQQSTSLLNDDVTPAAFWVTNPNNTIRHNAAAGGTHFGFWYRMNDHPDGPSFDRNICQKRIPLGEFFNNTVHSQGWFGLWIFEEYFPMQTGSCTSTVPVPAIFNSLTVWNCQKGAEWVNGGALQFHNFVMVNNNEAGIETKRILAPYVGGWGESNGAVIKNAKIVGHLDELGMGPTFCTSKGLVLPFSQGLTVSSVHFMNFDRHACVALGVTSITGVCNDRCGGWSAKFVGIRYFHAPNKGGFRWEHEAVLIDVDGSLTGHRGHTVVPHSSLLDPSHCTQEPAWSIGFPGSICDASVSFHRLAFNKPSPVSLLEKDVVLSDSFGTSIVPFQKKRLTHMSGWMALIPNANHINWYFKGVEHLTNISYTSTFYGFKEEDYVIISHNFTQNPDMFNVVDMRNGSANPLNWNSSKNGDWHLEANTSTLYYLVSGRSDLPQSQPISGTLDPGVKDVIINFQAYCCVLQDCFPVHPPSRKPIPRKRPAAYNLWSNESFWQSSPENNYTVPRPGANVIIPEGTWIVADVDIPPVERLIIWGVLEMEDKSEIGVAGPTYRRVVLNATYISVQGGRLIGGWEDNPFKGELQIVLRGNHSTPEWAFPDGPNQGAKVLGVFGELDLHGLPHSVYKTKLLETAEAGSKILSLVDAVDWQEGEDVVITTTSYDLHQTEIRRIAKILHGHKILILNDSLSYTHLAERQWISGTAQSYTLSADVGILSRNIKIVGDDYSVLSKDSFGARILVGSFTGNMMTFKGNARISNVEFHHSGQEGYRDSTDPRYAVTFLNLGQIQDHGLSYVRGCAFHHVFSPAIGVFGTDGVDIDDNIIYFTVGEGIRIWGDANRVRGNLVTLSVWPGTYQNRKDLSSTLWHAAIEINRGTNTVLQNNVVAGFGRVGYRIDGEPCSSQANSMENWFNNEAHGGLYGIYMNQDGLPGCSLIQGFTIWTCWDYGIYFQTTESVHIYNVTLVNNGMSIFSMVYMPPSVSHKISSKTVKIKNSLIVGSSPEFNCSDVLTNDSPDVELTSAHRSSRPPSGGRSGICWPTFASAHNMAPRKPHAGIMSYNAISGLLHVSDSTFVGFKDVCSGETNVIFITNPLNEDLQHPIHVKNVQLIDTIEQSKVFIHRPDISKVNPSDCVDMVCDAKRKSFLRDLDGSFLGNSGSVIPQAEYEWDGNSQLGIGDYRIPKAMLTYLNGSRIPVTEKAPHKGIIRDATCKYIPEWQSYQCSGMEYAMMVLESLDSDTETRRLSPVAIMSNGYVDLINGPQDHGWCAGYTCQRRLSLFHGIVALNKKYEVYFTGTSPQNLRLMLLNVEHNKAVLVGIFFSTLQRLDVYVNNSLVCPKNTAWNAQKKHCELERHLSTEQFLPNLGSTVPGENYFDRTYQMLYLFLKGTTPVEVHTATVIFVSFHLPVMTADEFFSSHNLVRNLALFLKIPSDKIRVSRIIGASLRKKRSTGHIMEFEIGAAPTQFLSNSTTGQMQLSELQEITDSLGQAVVLGKISTILGFNISSMSITSPIPQPTDSGWIKVTAQPVERSAFPVHYLALVSSLSVVAQPVAAQPGQPFPQQPSVKAVDPEGNCVSVGITSLTLKAILKDSNNNQVGGLSGNTTIPFSTCWANYTDLTPHRTGKNYKIEFVLDNTVRVDSRPFSLSAQSVPGGSGSSPGSGSSSSGHSKASSVGTPVQTLAVITACLVGRLLLLEVFMAAVFILNTTVGIN
Tissue specificity:
Induction:
Developmental stage:
Protein families: