Galactosidase alpha (4R19) Rabbit Monoclonal Antibody

Galactosidase alpha (4R19) Rabbit Monoclonal Antibody

Size1:50μl Price1:$138
Size2:100μl Price2:$240
Size3:500μl Price3:$980
SKU: AMRe11260 Category: Rabbit Monoclonal Antibody Tags: , ,

Datasheet

Summary

Production Name

Galactosidase alpha (4R19) Rabbit Monoclonal Antibody

Description

Rabbit Monoclonal Antibody

Host

Rabbit

Application

WB

Reactivity

Human

 

Performance

Conjugation

Unconjugated

Modification

Unmodified

Isotype

IgG

Clonality

Monoclonal

Form

Liquid

Storage

Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze/thaw cycles.

Buffer

Supplied in 50mM Tris-Glycine(pH 7.4), 0.15M NaCl, 40%Glycerol, 0.01% New type preservative N and 0.05% BSA.

Purification

Affinity purification

 

Immunogen

Gene Name

GLA

Alternative Names

Alpha gal A; GALA; Galactosidase, alpha; GLA; Melibiase;

Gene ID

2717

SwissProt ID

P06280

 

Application

Dilution Ratio

WB: 1:1000

Molecular Weight

49kDa

 

Background

Defects in GLA are the cause of Fabry disease (FD) [MIM:301500]. FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. The disease consists of an inborn error of glycosphingolipid catabolism. Catalyzes the hydrolysis of glycosphingolipids and participates in their degradation in the lysosome.

 

Research Area